spongiform encephalopathy

any one of a group of rapidly progressive degenerative neurological diseases that include scrapie in sheep, bovine spongiform encephalopathy (BSE) in cattle, and kuru, Creutzfeldt-Jakob disease, and Gerstmann-Straussler-Scheinker syndrome in humans. In humans the spongiform encephalopathies are characterized by rapidly progressive dementia associated with myoclonic jerks (see myoclonus); on pathological examination the brains of affected individuals show a characteristic cystic degeneration. The diseases are thought to be caused by unconventional transmissible agents (see prion).

The new mediacal dictionary. 2014.

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  • spongiform encephalopathy — n any of a group of degenerative diseases of the brain characterized by the development of spongiform lesions and by deterioration in neurological functioning see BOVINE SPONGIFORM ENCEPHALOPATHY, TRANSMISSIBLE SPONGIFORM ENCEPHALOPATHY * * * any …   Medical dictionary

  • spongiform encephalopathy — ˈspənjəˌfȯrm noun Etymology: spongiform resembling a sponge, from spongi + form : any of a group of degenerative diseases of the brain that are characterized by development of brain tissue having a structure like that of a porous sponge and by… …   Useful english dictionary

  • spongiform encephalopathy — noun Etymology: spongiform resembling a sponge, from Latin spongia + English iform Date: 1960 any of a group of degenerative diseases of the brain that are characterized by development of brain tissue having a structure like that of a porous… …   New Collegiate Dictionary

  • Transmissible spongiform encephalopathy — Transmissible spongiform encephalopathies (TSEs, also known as prion diseases) are a group of progressive conditions that affect the brain and nervous system of animals. According to the most widespread hypothesis they are transmitted by prions,… …   Wikipedia

  • Bovine spongiform encephalopathy — with BSE. A notable feature of such disease is the inability of the infected animal to stand.Source: APHIS] Bovine Spongiform Encephalopathy (BSE), commonly known as Mad Cow Disease (MCD), is a fatal, neurodegenerative disease in cattle, that… …   Wikipedia

  • Feline spongiform encephalopathy — is a disease that affects the brains and liversFact|date=January 2008 of felines. It is caused by proteins called prions.DiseaseFeline spongiform encephalopathy (FSE) is a prion disease thought to be related to Bovine spongiform encephalopathy… …   Wikipedia

  • bovine spongiform encephalopathy — n a fatal spongiform encephalopathy of cattle affecting the nervous system, resembling or identical with scrapie of sheep and goats, and prob. caused by a prion transmitted by infected tissue in food abbr. BSE called also mad cow disease * * * a… …   Medical dictionary

  • bovine spongiform encephalopathy — /spun jeuh fawrm / a fatal dementia of cattle, thought to be caused by the prion proteins implicated in Creutzfeldt Jakob disease. Also called mad cow disease. * * * ▪ pathology also called  mad cow disease        a fatal neurodegenerative… …   Universalium

  • transmissible spongiform encephalopathy — n any of a group of spongiform encephalopathies (as Creutzfeldt Jakob disease, kuru, and scrapie) that are now usu. considered to be caused and transmitted by prions * * * (TSE) prion disease …   Medical dictionary

  • bovine spongiform encephalopathy — noun Date: 1987 a fatal spongiform encephalopathy of cattle affecting the nervous system, resembling or identical with scrapie of sheep and goats, and probably caused by a prion transmitted by infected tissue in food abbreviation BSE; called also …   New Collegiate Dictionary

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